HEREDITARY GINGIVAL FIBROMATOSIS- A RARE AUTOSOMAL DOMINANT DISORDER

  • S. NVS Gottumukkala1, C D Dwarakanath2 , Suneetha K3 , Ramesh K S V4, G. S Penmetsa5, Satyanarayana B6

Abstract

Hereditary gingival fibromatosis is a rare autosomal dominant disorder occurring either as an isolated trait or as a manifestation of a systemic disorder or syndrome which is characterized by a generalized diffused involvement of the gingiva covering the entire surfaces of the crowns. The pathogenesis of the disease is still completely unclear, however mutations in the son of sevenless gene-1 (SOS-1) has been attributed for its occurrence in few forms of the disease. This paper discusses a case of a 13 year old female patient with generalized diffused gingival enlargement and a positive familial history. Though definitive treatment for the management of the condition is not available surgical gingivectomy with external bevel incision was performed and maintained for a period of 2yrs

Keywords: fibromatosis

Author Biography

S. NVS Gottumukkala1, C D Dwarakanath2 , Suneetha K3 , Ramesh K S V4, G. S Penmetsa5, Satyanarayana B6
  1. MDS, Associate professor, Dept of Periodontics, Vishnu Dental College, Bhimavaram.AP, India
  2. MDS, Professor and Head, Dept of Periodontics, Vishnu Dental College, Bhimavaram.AP, India
  3. MDS, Professor, Dept of Periodontics, Vishnu Dental College, Bhimavaram.AP, India
  4. MDS, Reader, Dept of Periodontics, Vishnu Dental College, Bhimavaram.AP, India
  5. MDS, Professor, Dept of Periodontics, Vishnu Dental College, Bhimavaram.AP, India
  6. MDS, PG Student, Dept of Periodontics, Vishnu Dental College, Bhimavaram.AP, India
Published
2017-04-28
How to Cite
Penmetsa5, Satyanarayana B6S. N. G. C. D. D. , S. K. , R. K. S. V. G. S. (2017). HEREDITARY GINGIVAL FIBROMATOSIS- A RARE AUTOSOMAL DOMINANT DISORDER. Journal of Biomedical and Pharmaceutical Research, 6(2). Retrieved from http://jbpr.in/index.php/jbpr/article/view/77
Section
Case Report